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Most cited papers in Systemic Sclerosis and Related Diseases

Systemic Sclerosis and Related Diseases

What are the most cited papers in Systemic Sclerosis and Related Diseases?

The most cited paper in Systemic Sclerosis and Related Diseases is "APACHE II-A Severity of Disease Classification System" (William A. Knaus, Elizabeth A. Draper, Douglas P. Wagner et al., 1986), with 13,426 citations. Next come "Evaluation of Diagnostic Criteria for Ankylosing Spondylitis" (5,762) and "Plasma Hsp90 levels in patients with systemic sclerosis and relation to lung and skin involvement: a cross-sectional and longitudinal study" (5,057).

Showing 50 of 98 papers. Every paper with more than 747 citations is listed.

Most cited papers, sortable by citations and release date
#Paper
1 APACHE II-A Severity of Disease Classification System William A. Knaus, Elizabeth A. Draper, Douglas P. Wagner et al. · Critical Care Medicine Aug 1986 13,426
2 Evaluation of Diagnostic Criteria for Ankylosing Spondylitis Sjef van der Linden, Hans A. Valkenburg, A. Cats · Arthritis & Rheumatism Apr 1984 5,762
3 Plasma Hsp90 levels in patients with systemic sclerosis and relation to lung and skin involvement: a cross-sectional and longitudinal study Hana Štorkánová, Sabína Oreská, Maja Špiritović et al. · Scientific Reports Open access 7 Jan 2021 5,057
4 Preliminary criteria for the classification of systemic sclerosis (scleroderma) Alfonse T. Masi · Arthritis & Rheumatism May 1980 4,957
5 Cellular and molecular mechanisms of fibrosis Thomas A. Wynn · The Journal of Pathology Open access 27 Dec 2007 4,557
6 An Official American Thoracic Society/European Respiratory Society Statement: Update of the International Multidisciplinary Classification of the Idiopathic Interstitial Pneumonias William David Travis et al. · American Journal of Respiratory and Critical Care Medicine Open access Sep 2013 4,352
7 A Phase 3 Trial of Pirfenidone in Patients with Idiopathic Pulmonary Fibrosis Talmadge E. King, Williamson Z. Bradford, Socorro Castro-Bernardini et al. · New England Journal of Medicine Open access 18 May 2014 4,051
8 Scleroderma (systemic sclerosis): classification, subsets and pathogenesis E. Carwile LeRoy, Casilda G. Black, Raúl Fleischmajer et al. Book chapter 6 Dec 2001 3,976
9 Mechanisms of fibrosis: therapeutic translation for fibrotic disease Thomas A. Wynn, Thirumalai R. Ramalingam · Nature Medicine Open access Jul 2012 3,589
10 2013 Classification Criteria for Systemic Sclerosis: An American College of Rheumatology/European League Against Rheumatism Collaborative Initiative Frank H J van den Hoogen et al. · Arthritis & Rheumatism Open access 3 Oct 2013 3,458
11 SYSTEMIC LUPUS ERYTHEMATOSUS DISEASE ACTIVITY INDEX Dafna D. Gladman, Dominique Ibañez, Murray B. Urowitz · Elsevier eBooks Book chapter 2007 2,977
12 Wegener Granulomatosis: An Analysis of 158 Patients Gary Stuart Hoffman, Gail S. Kerr, Randi Y. Leavitt et al. · Annals of Internal Medicine 15 Mar 1992 2,881
13 Idiopathic Pulmonary Fibrosis (an Update) and Progressive Pulmonary Fibrosis in Adults: An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline Ganesh Raghu et al. · American Journal of Respiratory and Critical Care Medicine Open access 29 Apr 2022 2,844
14 Rituximab versus Cyclophosphamide for ANCA-Associated Vasculitis John H. Stone et al. · New England Journal of Medicine Open access 14 Jul 2010 2,775
15 2019 European League Against Rheumatism/American College of Rheumatology Classification Criteria for Systemic Lupus Erythematosus Martin Aringer et al. · Arthritis & Rheumatology Open access 6 Aug 2019 2,644
16 Development of Autoantibodies before the Clinical Onset of Systemic Lupus Erythematosus Melissa R. Arbuckle, Micah T. McClain, Mark V. Rubertone et al. · New England Journal of Medicine Open access 15 Oct 2003 2,612
17 The development and initial validation of the systemic lupus international collaborating clinics/American college of rheumatology damage index for systemic lupus erythematosus Dafna D. Gladman et al. · Arthritis & Rheumatism Open access Mar 1996 2,609
18 Nintedanib in Progressive Fibrosing Interstitial Lung Diseases Kevin R. Flaherty, Athol Umfrey Wells, Vincent Cottin et al. · New England Journal of Medicine Open access 29 Sep 2019 2,440
19 Chronic graft-versus-host syndrome in man Howard M. Shulman, Keith M. Sullivan, Paul L. Weiden et al. · The American Journal of Medicine Aug 1980 2,436
20 Systemic sclerosis Christopher P. Denton, Dinesh Khanna · The Lancet 13 Apr 2017 2,230
21 Mixed connective tissue disease-an apparently distinct rheumatic disease syndrome associated with a specific antibody to an extractable nuclear antigen (ENA) Gordon C. Sharp, William S. Irvin, Eng M. Tan et al. · The American Journal of Medicine Feb 1972 1,855
22 Rituximab versus Cyclophosphamide in ANCA-Associated Renal Vasculitis Rachel Bronwen Jones, Jan Willem Cohen Tervaert, Thomas Häuser et al. · New England Journal of Medicine Open access 14 Jul 2010 1,759
23 Pathologic Classification of Diabetic Nephropathy Thijs W. Cohen Tervaert, Antien L. Mooyaart, Kerstin Amann et al. · Journal of the American Society of Nephrology 18 Feb 2010 1,724
24 Epidemiology and Estimated Population Burden of Selected Autoimmune Diseases in the United States Denise L. Jacobson, Stephen J. Gange, Noel R. Rose et al. · Clinical Immunology and Immunopathology Open access Sep 1997 1,686
25 Cyclophosphamide versus Placebo in Scleroderma Lung Disease Donald P. Tashkin et al. · New England Journal of Medicine Open access 21 Jun 2006 1,683
26 The classification of glomerulonephritis in systemic lupus erythematosus revisited Jan J. Weening et al. · Kidney International Open access 8 Jan 2004 1,678
27 Nintedanib for Systemic Sclerosis–Associated Interstitial Lung Disease Oliver Distler, Kristin B. Highland, Martina Gahlemann et al. · New England Journal of Medicine Open access 20 May 2019 1,667
28 Remodeling and homeostasis of the extracellular matrix: implications for fibrotic diseases and cancer Thomas R. Cox, Janine Terra Erler · Disease Models & Mechanisms Open access 15 Feb 2011 1,609
29 Changes in causes of death in systemic sclerosis, 1972–2002 V. Steen, Thomas A. Medsger · Annals of the Rheumatic Diseases Open access Mar 2007 1,540
30 The Management of Thrombosis in the Antiphospholipid-Antibody Syndrome Munther A. Khamashta, María José Cuadrado, Fedza Mujic et al. · New England Journal of Medicine Open access 13 Apr 1995 1,475
31 Common and unique mechanisms regulate fibrosis in various fibroproliferative diseases Thomas A. Wynn · Journal of Clinical Investigation Open access Mar 2007 1,474
32 Causes and risk factors for death in systemic sclerosis: a study from the EULAR Scleroderma Trials and Research (EUSTAR) database A. J. Tyndall et al. · Annals of the Rheumatic Diseases Open access 15 Jun 2010 1,461
33 Prevalence and Correlates of Accelerated Atherosclerosis in Systemic Lupus Erythematosus Mary J. Roman, Beth‐Ann Shanker, Adrienne Davis et al. · New England Journal of Medicine Open access 17 Dec 2003 1,430
34 Criteria for the classification of early systemic sclerosis. E. Carwile LeRoy, Thomas A. Medsger · PubMed Jul 2001 1,403
35 Morbidity and Mortality in Systemic Lupus Erythematosus During a 10-Year Period Ricard Cervera, Munther A. Khamashta, Josep Font et al. · Medicine Open access Sep 2003 1,392
36 Scleroderma Armando Gabrielli, Enrico Vittorio Avvedimento, Thomas M. Krieg · New England Journal of Medicine 6 May 2009 1,391
37 Development and validation of a consensus methodology for the classification of the ANCA-associated vasculitides and polyarteritis nodosa for epidemiological studies Richard Watts, Suzanne E. Lane, Thomas Hanslik et al. · Annals of the Rheumatic Diseases Open access 10 Aug 2006 1,375
38 A Multidimensional Index and Staging System for Idiopathic Pulmonary Fibrosis Brett Ley, Christopher J. Ryerson, Eric Vittinghoff et al. · Annals of Internal Medicine 15 May 2012 1,350
39 Incidence and Prevalence of Idiopathic Pulmonary Fibrosis Ganesh Raghu, Derek A. Weycker, John Edelsberg et al. · American Journal of Respiratory and Critical Care Medicine 30 Jun 2006 1,326
40 Transforming growth factor–β in tissue fibrosis Nikolaos G. Frangogiannis · The Journal of Experimental Medicine Open access 25 Dec 2019 1,322
41 Idiopathic Pulmonary Fibrosis: Clinical Relevance of Pathologic Classification Anna-Luise A. Katzenstein, Jeffrey L. Myers · American Journal of Respiratory and Critical Care Medicine Apr 1998 1,270
42 Modification and validation of the Birmingham Vasculitis Activity Score (version 3) Chetan B. Mukhtyar, R Lee, Denise Scott Brown et al. · Annals of the Rheumatic Diseases 3 Dec 2008 1,253
43 Interstitial Lung Disease in Systemic Sclerosis Nicole S L Goh, Sujal R. Desai, Srihari Veeraraghavan et al. · American Journal of Respiratory and Critical Care Medicine 27 Mar 2008 1,209
44 Exosomes/microvesicles as a mechanism of cell-to-cell communication Giovanni Camussi, Maria Chiara Deregibus, Stefania Bruno et al. · Kidney International Open access 11 Aug 2010 1,189
45 The natural history of multiple sclerosis:a geographically based study David A. Cottrell, Marcelo Kremenchutzky, George P. Rice et al. · Brain Apr 1999 1,170
46 Systemic sclerosis: a prototypic multisystem fibrotic disorder John Varga, David Abraham · Journal of Clinical Investigation Open access Mar 2007 1,166
47 Update of EULAR recommendations for the treatment of systemic sclerosis Otylia Kowal‐Bielecka et al. · Annals of the Rheumatic Diseases Open access135 authors 10 Nov 2016 1,129
48 The prevalence of MS in the United States Mitchell Taylor Wallin, William J. Culpepper, Jonathan D. Campbell et al. · Neurology Open access 15 Feb 2019 1,128
49 Pathologic observations in systemic sclerosis (scleroderma) William D’Angelo, James F. Fries, Alfonse T. Masi et al. · The American Journal of Medicine Mar 1969 1,123
50 An official European Respiratory Society/American Thoracic Society research statement: interstitial pneumonia with autoimmune features Aryeh Fischer, Katerina M. Antoniou, Kevin M. Brown et al. · European Respiratory Journal 9 Jul 2015 1,111

Citations are OpenAlex's own counts, from its 2026-09-23 snapshot, so the ranking can differ from Google Scholar or Web of Science. A paper is listed for a field when OpenAlex files it under one of the field's topics; retracted papers and papers whose citation count cannot be traced to citing works are left out, and a preprint and the article it became are shown once. Release dates are OpenAlex's: where a source gave only a month or a year, that is what is shown. How the lists are chosen.